Susac Syndrome
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- Gerard Espinosa
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- Hospital Clinic Barcelona
Research Output:
Chapter in Book/Report/Conference proceeding
Chapter
Peer-reviewPublication Information
Output type
Research Output:
Chapter in Book/Report/Conference proceeding
Chapter
Peer-reviewHost publication Subtitle
Systemic and Organ-specific Diseases, Second EditionOriginal language
EnglishPages from-to (Number of pages)
Pages 167-171 (5 pages)Publication milestones
- Published - 01/01/2025
Publication status
Published - 01/01/2025
Publisher
Springer Nature, United StatesISBN (Print)
9783031698941ISBN (Electronic)
9783031698958Publication IDs
- Scopus: 105002537274
Host publication title
Autoimmune Disease DiagnosisAbstract
The Susac syndrome is a microangiopathy causing small infarcts in the brain, cochlea, and retina. It is characterized by the clinical triad of acute or subacute encephalopathy, sensorineural hearing loss, and retinal branch artery occlusions. This syndrome is probably an immune-mediated endotheliopathy that affects these organs’ microvasculature. The definite diagnosis is made by the presence of the triad of brain, retinal, and vestibulocochlear involvements. If only two domains are affected, a probable diagnosis can be proposed. Treatment of this condition includes immunosuppression with high-dose steroids and intravenous immunoglobulin, and in some cases cytotoxic drugs.